Hereditary hemorrhagic telangiectasia with a pulmonary arteriovenous fistula.
نویسندگان
چکیده
منابع مشابه
Asymptomatic pulmonary arteriovenous malformations in children with hereditary hemorrhagic telangiectasia.
BACKGROUND Children with Hereditary Hemorrhagic Telangiectasia (HHT) may have pulmonary arteriovenous malformations (AVMs), which can lead to symptoms of shortness of breath, exercise intolerance, clubbing, cyanosis and hemoptysis. However, some patients with pulmonary AVMs may be asymptomatic, placing them at risk for complications such as stroke or brain abscess if they are not identified and...
متن کاملRecurrent brain abscess: manifestation of pulmonary arteriovenous fistula and hereditary hemorrhagic telangiectasia.
A unique case of recurrent brain abscess as the primary manifestation of pulmonary arteriovenous fistula is presented. In the absence of hematologic abnormalities and characteristic physical findings, the diagnosis of pulmonary arteriovenous fistula is particularly elusive. Patients with brain abscess must be carefully evaluated for the presence of pulmonary arteriovenous fistula or hereditary ...
متن کاملLife-threatening pulmonary hemorrhage with pulmonary arteriovenous malformations and hereditary hemorrhagic telangiectasia.
The occurrence of significant pulmonary hemorrhage associated with pulmonary arteriovenous malformations (PAVMs) and hereditary hemorrhagic telangiectasia (HHT) and the incidence of PAVMs in family members of patients with PAVMs and HHT are poorly defined. We reviewed our experience in 143 patients with PAVMs and HHT. Eleven (8 percent) of the 143 patients with HHT and PAVMs had a history of ei...
متن کاملHereditary Hemorrhagic Telangiectasia with Atypical Pulmonary Arteriovenous Malformation during Advanced Pregnancy - A Case Report
We described a case of a new, atypical pulmonary arteriovenous malformation (AVM) during advanced pregnancy, in a previously well screened woman with known hereditary hemorrhagic telangiectasia (HHT) and a remote history of pulmonary AVM embolization. A 29-year old woman, gravida 3, para 2, at 35 weeks' gestation was admitted following a first episode of massive hemoptysis. Pulmonary angiograph...
متن کاملPulmonary arterial hypertension in a patient with hereditary hemorrhagic telangiectasia.
Hereditary hemorrhagic telangiectasia (HHT) is an autosomal dominant disorder characterized by the triad of epistaxis, telangiectasia and vascular malformations. Pulmonary vascular complications associated with this disease include pulmonary arteriovenous malformations (AVM) and, less frequently, pulmonary hypertension (PH). We report the case of a patient who presented multiple pulmonary AVM a...
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ژورنال
عنوان ژورنال: Japanese Circulation Journal
سال: 1984
ISSN: 0047-1828,1347-4839
DOI: 10.1253/jcj.48.1087